REVEAL Registry Risk Score for Pulmonary Arterial Hypertension (PAH)Loading...WHO group 1 subgroupOther0Associated PAH-connective tissue disease+1Associated PAH-portpulmonary hypertension+2Familial PAH+2Renal insufficiencyNo0Yes+1Male age > 60 yearsNo0Yes+2NYHA/WHO functional classI-2II0III+1IV+2Systolic BP, mmHg≤ 920> 92+16-minute walk test≥ 440 m-1165-440 m0< 165 m+1BNP*, pg/mL< 50-250-1800> 180+1Pericardial effusion on echocardiogramNo0Yes+1DLCO on pulmonary function test≥ 80%-133-79%0≤ 32%+1Mean right atrial pressure > 20 mmHg within 1 year on right heart catheterizationNo0Yes+1Pulmonary vascular resistance > 32 wood units on right heart catherizationNo0Yes+2